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MDK-NITISINONE 5 MG

NITISINONE : 5 MG · DIN 02457725 · MENDELIKABS INC

Health Canada status: MARKETED

What is MDK-NITISINONE?

MDK-NITISINONE 5 MG contains NITISINONE : 5 MG. It is listed in the Health Canada Drug Product Database under DIN 02457725, held by MENDELIKABS INC, supplied as CAPSULE for ORAL administration. Health Canada currently lists it as marketed, status dated 20-Oct-2016. Nexara Health is a licensed Canadian wholesale distributor (DEL 3-002896-A) and can source this product for hospitals, pharmacies and clinics. Availability and lead time are confirmed per order.

What is MDK-NITISINONE used for?

Treatment of hereditary tyrosinemia type 1 (HT-1) in combination with dietary restriction of tyrosine and phenylalanine.

Authorized indication as written in the Health Canada product monograph. For healthcare professionals and licensed purchasers; this is not medical advice.

Product details and regulatory record

DIN02457725
Brand nameMDK-NITISINONE
Generic / active ingredientNITISINONE : 5 MG
ManufacturerMENDELIKABS INC
Strength5 MG
Dosage formCAPSULE
Route of administrationORAL
SchedulePrescription
ATC codeA16AX04 NITISINONE
AHFS class92:92.00
BiosimilarNo
Health Canada statusMARKETED
Status date20-Oct-2016
Original market date2016-10-20 00:00:00

How is it administered?

Initial dose: 1 mg/kg/day divided in 2 oral doses. Adjust to 1.5-2 mg/kg/day based on succinylacetone levels and biochemical parameters. Maintain consistent routine regarding food intake.

Included because it drives pack selection and wastage. Consult the monograph.

How is it stored and handled?

Store refrigerated (2-8°C). After opening, 2mg capsules stable at room temp (≤25°C) for 1 month; 5, 10, 20mg capsules stable for 3 months.

How is it supplied?

Hard gelatin capsules (2 mg, 5 mg, 10 mg, 20 mg). Specific bottle sizes not listed in provided text.

Contraindications

Hypersensitivity to nitisinone or any ingredient in the formulation. Mothers receiving MDK-Nitisinone should not breast feed.

Warnings and precautions

Elevated plasma tyrosine levels (maintain <500 μmol/L via diet); leucopenia and thrombocytopenia (monitor blood counts); risk of hepatic malignancy; ocular toxicity; developmental delay.

What can be used instead?

Other Canadian products sharing ATC code A16AX04 NITISINONE. 8 of 12 DINs in this group are currently marketed — marketed products are listed first, because that is what can actually be bought. These tables describe supply, not clinical equivalence: substitution rests with the prescriber or pharmacist, and interchangeability is determined provincially.

ProductStrengthFormManufacturerHealth Canada statusDIN
MDK-NITISINONE10 MGCAPSULEMENDELIKABS INCMARKETEDDIN 02457733
MDK-NITISINONE2 MGCAPSULEMENDELIKABS INCMARKETEDDIN 02457717
ORFADIN10 MGCAPSULESWEDISH ORPHAN BIOVITRUM AB (PUBL)MARKETEDDIN 02459728
ORFADIN2 MGCAPSULESWEDISH ORPHAN BIOVITRUM AB (PUBL)MARKETEDDIN 02459698
ORFADIN20 MGCAPSULESWEDISH ORPHAN BIOVITRUM AB (PUBL)MARKETEDDIN 02459736
ORFADIN4 MGSUSPENSIONSWEDISH ORPHAN BIOVITRUM AB (PUBL)MARKETEDDIN 02469693
ORFADIN5 MGCAPSULESWEDISH ORPHAN BIOVITRUM AB (PUBL)MARKETEDDIN 02459701
MDK-NITISINONE20 MGCAPSULEMENDELIKABS INCDORMANTDIN 02470055
NITISINONE TABLETS10 MGTABLETCYCLE PHARMACEUTICALS LTD.CANCELLED POST MARKETDIN 02458632
NITISINONE TABLETS2 MGTABLETCYCLE PHARMACEUTICALS LTD.CANCELLED POST MARKETDIN 02458616

Who else supplies NITISINONE worldwide?

Nexara tracks national medicine registries and published price lists across multiple markets. NITISINONE appears in 51 registered pack listings across 6 markets, published on 6 different national price bases. Where a Canadian route is closed, that is where an alternative route of supply starts — subject to the import rules in both countries.

Registered listings are not stock. Ask us to confirm what can actually be sourced for your order.

How can I get it?

Nexara Health supplies this product to licensed Canadian buyers — pharmacies, hospitals, clinics, licensed distributors, and clinical trial sponsors or their CROs. We confirm stock, pack size, expiry and pricing at the time of quotation. If the product is on backorder or in shortage, we identify equivalent alternatives and import options where permitted.

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Ordering questions

Who can buy this from Nexara?

Licensed entities only. Nexara holds Health Canada establishment licence DEL 3-002896-A and ships only to a licensed address.

Is there a minimum order?

Yes, set per product line and per pack multiple rather than on the order total, so you are never asked to buy a part-pack. The minimum for this line is confirmed with your quote.

What is the lead time?

Confirmed per order at quotation, and it depends on current stock position and whether the product is in shortage.

Can Nexara supply this for a clinical trial?

Yes — comparator and background-therapy supply, including sourcing from other markets where a Canadian pack will not satisfy the protocol. Clinical trial supply.

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Health Canada Drug Product Database (DPD), DIN 02457725. Last reviewed 2026-09-08. Nexara Health is a licensed wholesaler and supplies licensed entities only; consumer orders are routed to a partner pharmacy.